{"id":13530,"date":"2026-02-20T15:34:14","date_gmt":"2026-02-20T15:34:14","guid":{"rendered":"https:\/\/www.europesays.com\/be-fr\/13530\/"},"modified":"2026-02-20T15:34:14","modified_gmt":"2026-02-20T15:34:14","slug":"haute-autorite-de-sante-evaluation-des-denrees-alimentaires-destinees-a-des-fins-medicales-speciales-pour-la-prise-en-charge-nutritionnelle-des-maladies-rares-hereditaires-du-metabolisme","status":"publish","type":"post","link":"https:\/\/www.europesays.com\/be-fr\/13530\/","title":{"rendered":"Haute Autorit\u00e9 de Sant\u00e9 &#8211; \u00c9valuation des denr\u00e9es alimentaires destin\u00e9es \u00e0 des fins m\u00e9dicales sp\u00e9ciales pour la prise en charge nutritionnelle des maladies rares h\u00e9r\u00e9ditaires du m\u00e9tabolisme"},"content":{"rendered":"<p>  Haute Autorit\u00e9 de Sant\u00e9 &#8211; \u00c9valuation des denr\u00e9es alimentaires destin\u00e9es \u00e0 des fins m\u00e9dicales sp\u00e9ciales pour la prise en charge nutritionnelle des maladies rares h\u00e9r\u00e9ditaires du m\u00e9tabolisme &#8211; note de cadrage<\/p>\n<p><a id=\"top\" style=\"display:block;\"\/><br \/>\n&#13;<br \/>\n&#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n&#13;<\/p>\n<p>&#13;<\/p>\n<p>&#13;<\/p>\n<p>            &#13;<\/p>\n<p>   <a id=\"toc_1_1_1\" class=\"anchor toc-anchor\"\/><br \/>\n   Contexte<\/p>\n<p>Suite \u00e0 une saisine du minist\u00e8re charg\u00e9 de la sant\u00e9, la HAS va \u00e9valuer les modalit\u00e9s de prise en charge des denr\u00e9es alimentaires destin\u00e9es \u00e0 des fins m\u00e9dicales sp\u00e9ciales (DADFMS) n\u00e9cessaires \u00e0 la suppl\u00e9mentation nutritionnelle des personnes atteintes de maladies rares h\u00e9r\u00e9ditaires du m\u00e9tabolisme (MHM).<\/p>\n<p>Actuellement, la distribution de ces DADFMS est centralis\u00e9e par le service de la r\u00e9trocession de l\u2019Agence g\u00e9n\u00e9rale des \u00e9quipements et produits de sant\u00e9 (AGEPS) pour les patients pr\u00e9sents en France (m\u00e9tropolitaine et DROM-COM) dans le cadre d\u2019un dispositif d\u00e9rogatoire mis en place depuis 1983.<\/p>\n<p>\u00a0<\/p>\n<p><a id=\"toc_1_1_2\" class=\"anchor toc-anchor\"\/><br \/>\n   Enjeu<\/p>\n<p>L\u2019enjeu consiste \u00e0 d\u00e9terminer la faisabilit\u00e9 et le cas \u00e9ch\u00e9ant, d\u00e9finir des modalit\u00e9s de prise en charge \u00e0 travers la LPPR (liste des produits et prestations remboursables) pour permettre la distribution de ces DADFMS par les diff\u00e9rents acteurs autoris\u00e9s par la r\u00e9glementation.<\/p>\n<p>\u00a0<\/p>\n<p><a id=\"toc_1_1_3\" class=\"anchor toc-anchor\"\/><br \/>\n   M\u00e9thode de travail envisag\u00e9e<\/p>\n<p>Cette \u00e9valuation reposera sur\u00a0:<\/p>\n<p>    Une analyse de la litt\u00e9rature scientifique pertinente identifi\u00e9e apr\u00e8s une recherche documentaire syst\u00e9matique\u00a0;<br \/>\n    Une analyse des donn\u00e9es fournies par les repr\u00e9sentants des industriels\u00a0;<br \/>\n    Un recueil de la position des parties prenantes, \u00e0 savoir\u00a0les organisations professionnelles et les associations de patients.<\/p>\n<p>\u00a0<\/p>\n<p>    <a id=\"ancreDocAss\" class=\"anchor toc-anchor\"\/><\/p>\n<p>        Nous contacter<\/p>\n<p>Contact \u00e9valuation des dispositifs<\/p>\n<p>&#13;<\/p>\n<p>&#13;<\/p>\n<p>&#13;<br \/>\n&#13;<br \/>\n&#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n  &#13;<br \/>\n&#13;<br \/>\n&#13;<br \/>\n&#13;<br \/>\n&#13;<br \/>\n&#13;<br \/>\n&#13;<\/p>\n<p>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<\/p>\n<p>zJy1xTjrvP3FWrs6<\/p>\n<p>&#13;<br \/>\n&#13;<\/p>\n<p>    <img decoding=\"async\" src=\"https:\/\/www.has-sante.fr\/images\/jalios\/icons\/ajax-wait.svg\" class=\"jalios-icon ajax-wait jalios-icon-svg\" alt=\"\" id=\"ajaxWaitIcon\"\/><br \/>\n  &#13;<br \/>\n   &#13;<br \/>\n&#13;<\/p>\n","protected":false},"excerpt":{"rendered":"Haute Autorit\u00e9 de Sant\u00e9 &#8211; \u00c9valuation des denr\u00e9es alimentaires destin\u00e9es \u00e0 des fins m\u00e9dicales sp\u00e9ciales pour la prise&hellip;\n","protected":false},"author":2,"featured_media":13531,"comment_status":"","ping_status":"","sticky":false,"template":"","format":"standard","meta":{"footnotes":""},"categories":[82],"tags":[8523,8539,8526,8534,3345,12,13,18,17,8530,8522,8533,8537,8336,8528,8529,86,8535,828,4376,8531,8524,8532,8540,8536,8521,87,8527,8525,8538],"class_list":{"0":"post-13530","1":"post","2":"type-post","3":"status-publish","4":"format-standard","5":"has-post-thumbnail","7":"category-sante","8":"tag-accreditation-medecins","9":"tag-aides-techniques","10":"tag-ald","11":"tag-alimentation-et-sommeil","12":"tag-assurance-maladie","13":"tag-be","14":"tag-be-fr","15":"tag-belgique","16":"tag-belgium","17":"tag-certification","18":"tag-certification-etablissements","19":"tag-commission-transparence","20":"tag-congenitales","21":"tag-evaluation","22":"tag-has","23":"tag-haute-autorite-de-sante","24":"tag-health","25":"tag-maladies-genetiques","26":"tag-medicaments","27":"tag-metabolisme","28":"tag-patient","29":"tag-pratiques-professionnelles","30":"tag-qualite-soins","31":"tag-rapports-daposevaluation-des-technologies-de-sante","32":"tag-rares","33":"tag-recommandations","34":"tag-sante","35":"tag-service-medical-rendu","36":"tag-soins-medicaux","37":"tag-toutes-nos-publications"},"share_on_mastodon":{"url":"","error":""},"_links":{"self":[{"href":"https:\/\/www.europesays.com\/be-fr\/wp-json\/wp\/v2\/posts\/13530","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/www.europesays.com\/be-fr\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/www.europesays.com\/be-fr\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/www.europesays.com\/be-fr\/wp-json\/wp\/v2\/users\/2"}],"replies":[{"embeddable":true,"href":"https:\/\/www.europesays.com\/be-fr\/wp-json\/wp\/v2\/comments?post=13530"}],"version-history":[{"count":0,"href":"https:\/\/www.europesays.com\/be-fr\/wp-json\/wp\/v2\/posts\/13530\/revisions"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/www.europesays.com\/be-fr\/wp-json\/wp\/v2\/media\/13531"}],"wp:attachment":[{"href":"https:\/\/www.europesays.com\/be-fr\/wp-json\/wp\/v2\/media?parent=13530"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/www.europesays.com\/be-fr\/wp-json\/wp\/v2\/categories?post=13530"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/www.europesays.com\/be-fr\/wp-json\/wp\/v2\/tags?post=13530"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}